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MetabERN - Education

Share information and documentation with actors involved in the field of hereditary metabolic disorders

Home > Resources > Apps > Isovaleric Acidemia (IVA) App

Isovaleric Acidemia (IVA) App

Metabolic Diet App

Isovaleric Acidemia (IVA) App

is a genetic disorder caused by a deficiency in the isovaleryl-CoA dehydrogenase (IVD) enzyme.

Patients are prescribed a protein and Leu restricted diet to prevent high levels of Isovaleric acid.

This App is designed to support families and children with IVA on protein restricted diets.